Malignant triton tumor in the mandibular and cervical region

Authors

Keywords:

malignant triton tumor, rhabdomyoblasts, mandible.

Abstract

Introduction: Malignant triton tumor is a rare neoplasm in which rhabdomyoblasts are present in a malignant tumor of the peripheral nerve sheath. This condition is characterized by its aggressiveness and bad prognosis. Location in the head and neck is infrequent. Immunohistochemical testing plays an important role in its diagnosis.

Objective: Describe an unusually large malignant triton tumor.

Case presentation: A case is presented of a female 16-year-old patient referred to the maxillofacial surgery service of the National Institute of Pediatrics in Mexico City with a diagnosis of neuroectodermal tumor of one year's evolution in the facial and cervical region. In clinical terms, the tumor was exophytic, multilobed, with extensive areas of necrosis, a surface in several shades of color and an approximate size of 18 x 10 x 12 cm. Biopsy and immunohistochemical testing confirmed the diagnosis of malignant triton tumor. The patient underwent surgery in which the lesion was totally excised with a safety margin. Evolution was clumsy, with a fatal outcome at six months of treatment.

Conclusions: Triton tumor is an aggressive neoplasm whose early detection makes it possible for surgeons to provide an appropriate treatment.

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Author Biographies

Pedro Jorge Téllez Rodríguez, Instituto Nacional de Pediatría, Servicio de Cirugía Oral y Maxilofacial. Ciudad de México, México.

  • Jefe del servicio de cirugía máxilo facial del Instituto Nacional de Pediatría
  • Adscrito del Instituto Nacional de Pediatría
  • Cirugía Maxilofacial Pediátrica con Ced. Prof. 852862

Rubí López Fernández, Instituto Nacional de Pediatría, Servicio de Cirugía Oral y Maxilofacial. Ciudad de México, México.

Instituto Nacional de Pediatría, Servicio de Cirugía Oral y Maxilofacial. Ciudad de México, México

Mario Alberto Lagunes López, Instituto Nacional de Pediatría, Servicio de Cirugía Oral y Maxilofacial. Ciudad de México, México.

Alta Especialidad en Medicina en Cirugía Rino-Máxilo-Facial2015-2016 | Hospital Ángeles de Puebla/UNAMGalardonado con el premio “Mario Scarrone” por la ALACIBU en el cono norte como el residente más distinguido, obteniendo la más alta calificación en evaluación curricular en Latinoamérica Especialidad en Cirugía Oral y Maxilofacial2011-2015 | Hospital Regional 1° de Octubre ISSSTE/UNAMGraduado con mención honorífica hospitalaria y universitaria.Certificado por el Consejo Mexicano de Cirugía Oral y Maxilofacial, obteniendo el 1er lugar nacional en los exámenes de certificación. Licenciatura en Estomatología 2004-2010 | BUAP

Carlos Guillermo Camacho Olguín, Instituto Nacional de Oncología y Radiobiología, Servicio de Cirugía Oncológica de Cabeza y Cuello. La Habana, Cuba.

Egresado de laFacultad de Ciencias  Medicas de la UAEH en el 2009.

Diplomado por la UNAM / CIORE en Implantología General y Rehabilitación, y en Relaciones interpersonales y Filosofía Existencial Enfocada al Desarrollo Humano por la SEP.

Primer Grado en Cirugía Maxilofacial en el Hospital General Calixto Garcia de La Habana, Cuba.

Grado Médico en Cirugía Oncológica de Cabeza y Cuello en el Instituto Nacional de Oncología y Rediobiología de La Habana, Cuba.

Certificado por el Consejo Mexicano de Cirugía Maxilofacial

Principales líneas de investigación: Neoplasias de cabeza y Cuello y Trauma Maxilofacial


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Published

2021-12-14

How to Cite

1.
Téllez Rodríguez PJ, López Fernández R, Lagunes López MA, Camacho Olguín CG, Rodríguez Jurado R, Hernández Bringas O. Malignant triton tumor in the mandibular and cervical region. Rev Cubana Estomatol [Internet]. 2021 Dec. 14 [cited 2025 Feb. 22];58(4):e3198. Available from: https://revestomatologia.sld.cu/index.php/est/article/view/3198

Issue

Vol. 58 No. 4 (2021): OCT- DEC

Section

Case Report

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